Expanding the genetic spectrum of the pyruvate carboxylase deficiency with novel missense, deep intronic and structural variants.

Journal Information

Full Title: Mol Genet Metab Rep

Abbreviation: Mol Genet Metab Rep

Country: Unknown

Publisher: Unknown

Language: N/A

Publication Details

Subject Category: Genetics & Heredity

Available in Europe PMC: Yes

Available in PMC: Yes

PDF Available: No

Transparency Score
4/6
66.7% Transparent
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Core Indicators
Evidence found in paper:

"the novel variants were classified according to acmg recommendations [ ] and submitted to the clinvar database ( https://www ncbi nlm nih gov/clinvar/ ) (accession numbers: scv002003956 - scv002003961) 2 6 cytogenetic analysis of patient 1 and his parents was performed on gtg-banded metaphase chromosomes obtained from cultured peripheral blood lymphocytes according to standard procedures."

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Evidence found in paper:

"Declaration of Competing Interest All authors have seen and approved the manuscript. All authors declare no conflict of interest."

Evidence found in paper:

"Funding The research was carried out within the state assignment of the Ministry of Science and Higher Education of the Russian Federation for RCMG."

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Open Access
Paper is freely available to read
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Assessment Info

Tool: rtransparent

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Last Updated: Aug 05, 2025